245 Rapidly Progressing Non-IgG4-Related Sclerosing Mediastinitis

IgG4-related sclerosing disease.

Based on histological and immunohistochemical examination of various organs of patients with autoimmune pancreatitis (AIP), a novel clinicopathological entity of IgG4-related sclerosing disease has been proposed. This is a systemic disease that is characterized by extensive IgG4-positive plasma cells and T-lymphocyte infiltration of various organs. Clinical manifestations are apparent in the pa...

IgG4-related sclerosing cholangitis.

IgG4-Related Sclerosing Mesenteritis

© 2016 The Korean Society of Pathologists/The Korean Society for Cytopathology This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/ by-nc/3.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited. pISSN 2383-7...

IgG4-Related Chronic Sclerosing Dacryoadenitis

dilated fundus examination findings were normal. Blood studies were negative for antinuclear antibodies and rheumatoid factors and showed a normal complete blood count and negative angiotensin-converting enzyme levels. We diagnosed bilateral atypical Cogan syndrome in the patient. The bilateral iritis resolved with cycloplegics and topical steroid drops. The patient has been referred for a coch...

IgG4-Related Sclerosing Mediastinitis: Report of a Case with Distinct Ultrasound Findings.

elevated, but the absence of such elevated values does not rule out the disease. The exact role of IgG4 in these patients has not been elucidated so far. The triggers and pathogenesis of IgG4-related disease are still unknown. Interestingly, in contrast to autoimmune diseases which often occur in women, IgG4-related disease predominantly affects middle-aged and elderly men (I. Novotny et al. Di...